RT  - European Journal of Gynaecological Oncology
ID  - 10.12892/ejgo3510.2017
T1  - Retroperitoneal primitive neuroectodermal tumor (PNET): case report and review of literature
A1  - A. Koch
A1  - S. Frigo
A1  - L. Lecointre
A1  - M. Humme
A1  - C.Y. Akladios
A1  - J.P. Bergerat
A1  - G. Noë
A1  - A. Wattiez
K1  - Primitive neuroectodermal tumor; PNET; Retroperitoneal; Ewing’s tumor.
YR  - 2017
SP  - 314
AB  - <p>Primitive Neuroectodermal tumor belongs to the family of Ewing’s tumor and is characterized by a t (11;22) (q24;q12) or a t (21;22) (q22;q12) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no specific characteristics for imaging. The diagnosis is made on histological examination of the surgical specimen or biopsies. Radiotherapy and chemotherapy complete the treatment. The authors report the case of a 26-year-old patient who only had pelvic discomfort. Diagnostic laparoscopy showed a retroperitoneal and retrovesical mass of five centimeters. The patient benefited from adjuvant chemotherapy and radiotherapy. She is free of disease 30 months after treatment.</p>