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Desmoplastic small round cell tumor (DSRCT) arising in the ovary: report of a case diagnosed at an early stage and review of the literature

  • G. D’Ippolito1,2
  • M.T. Huizing3
  • W.A.A. TJALMA2,*,

1Department of Obstetrics and Gynecology, University of Modena and Reggio Emilia, Modena, Italy

2Department of Gynecological Oncology, B-2650 Edegem, Belgium

3Department of Medical Oncology, University Multidisciplinary Breast and Pelvic Gynecological Oncology Clinic, Antwerp University Hospital, Edegem, Belgium

DOI: 10.12892/ejgo20120196 Vol.33,Issue 1,January 2012 pp.96-100

Published: 10 January 2012

*Corresponding Author(s): W.A.A. TJALMA E-mail:


Background: Desmoplastic small round cell tumor (DSRCT) is a rare sarcoma tumor affecting mainly young adult males. It rarely has an ovarian involvement. Case: A 29-year-old woman presented to her gynecologist for amenorrhoea. The laboratory results demonstrated a menopausal status and the ultrasound revealed a large mass of the right ovary. The right ovary was completely removed by laparoscopy. Pathology, cytology and immunochemistry revealed a DSRCT. In January 2009 a left salpingo-oophorectomy and a right salpingectomy were performed via laparoscopy. After 35 months from diagnosis there was no clinical evidence of disease recurrence. Conclusion: DSRCT is a rare ovarian tumor in adolescence with a general poor outcome. Every ovarian mass regardless of age should be approached with caution.


Desmoplastic small round cell tumor; Ovarian neoplasm; Early stage tumor; Treatment; Good response

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G. D’Ippolito,M.T. Huizing,W.A.A. TJALMA. Desmoplastic small round cell tumor (DSRCT) arising in the ovary: report of a case diagnosed at an early stage and review of the literature. European Journal of Gynaecological Oncology. 2012. 33(1);96-100.


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