Perivascular epithelial cell tumor arising from polypoid adenomyoma: a case report
1Department of Obstetrics and Gynecology, Shimane University School of Medicine, Izumo
2Department of Biochemistry, Shimane University School of Medicine, Izumo
3Department of Organ Pathology, Shimane University School of Medicine Izumo (Japan).
DOI: 10.12892/ejgo340122 Vol.34,Issue 1,January 2013 pp.104-106
Published: 10 January 2013
The present report describes a rare case of a uterine perivascular epithelioid cell tumor (PEComa) arising from a polypoid adenomyoma. The patient, a 44-year old woman with tuberous sclerosis, was incidentally found to have a uterine mass with malignantappearing features on a computed tomography (CT) scan. Pathological examination of the hysterectomy specimen demonstrated that the tumor was composed of pale, spindle-shaped, epithelioid tumor cells which were positive for SMA and HMB-45. These findings were consistent with a PEComa arising from a polypoid adenomyoma.
Perivascular epithelioid cell tumor (PEComa); Uterus; Polypoid adenomyoma.
T. Ishibashi,K. Nakayama,N. Nakayama,H. Katagiri,N. Ishikawa,K. Miyazaki. Perivascular epithelial cell tumor arising from polypoid adenomyoma: a case report. European Journal of Gynaecological Oncology. 2013. 34(1);104-106.
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