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Case Reports

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Perivascular epithelial cell tumor arising from polypoid adenomyoma: a case report

  • T. Ishibashi1
  • K. Nakayama1,*,
  • N. Nakayama2
  • H. Katagiri1
  • N. Ishikawa3
  • K. Miyazaki1

1Department of Obstetrics and Gynecology, Shimane University School of Medicine, Izumo

2Department of Biochemistry, Shimane University School of Medicine, Izumo

3Department of Organ Pathology, Shimane University School of Medicine Izumo (Japan).

DOI: 10.12892/ejgo340122 Vol.34,Issue 1,January 2013 pp.104-106

Published: 10 January 2013

*Corresponding Author(s): K. Nakayama E-mail: kn88@med.shimane-u.ac.jp

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Abstract

The present report describes a rare case of a uterine perivascular epithelioid cell tumor (PEComa) arising from a polypoid adenomyoma. The patient, a 44-year old woman with tuberous sclerosis, was incidentally found to have a uterine mass with malignantappearing features on a computed tomography (CT) scan. Pathological examination of the hysterectomy specimen demonstrated that the tumor was composed of pale, spindle-shaped, epithelioid tumor cells which were positive for SMA and HMB-45. These findings were consistent with a PEComa arising from a polypoid adenomyoma.

Keywords

Perivascular epithelioid cell tumor (PEComa); Uterus; Polypoid adenomyoma.

Cite and Share

T. Ishibashi,K. Nakayama,N. Nakayama,H. Katagiri,N. Ishikawa,K. Miyazaki. Perivascular epithelial cell tumor arising from polypoid adenomyoma: a case report. European Journal of Gynaecological Oncology. 2013. 34(1);104-106.

URL:

https://www.ejgo.net/articles/10.12892/ejgo340122

References

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