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Retroperitoneal primitive neuroectodermal tumor (PNET): case report and review of literature

  • A. Koch1,*,
  • S. Frigo1
  • L. Lecointre1
  • M. Humme1
  • C.Y. Akladios1
  • J.P. Bergerat2
  • G. Noë3
  • A. Wattiez1

1Department of Obstetrics and Gynecology, Strasbourg University Hospital, Schiltigheim, France

2Department of Oncology and Hematology, Strasbourg University Hospital, Strasbourg Cedex, France

3Department of Radiotherapy, Centre de lutte contre le cancer Paul Strauss, Strasbourg, France

DOI: 10.12892/ejgo3510.2017 Vol.38,Issue 2,April 2017 pp.314-318

Published: 10 April 2017

*Corresponding Author(s): A. Koch E-mail: antoine.koch@chru-strasbourg.fr

Abstract

Primitive Neuroectodermal tumor belongs to the family of Ewing’s tumor and is characterized by a t (11;22) (q24;q12) or a t (21;22) (q22;q12) translocation. Retroperitoneal primitive neuroectodermal tumor (PNET) are rare, usually affect young adults, and are often diagnosed late. There is no specific characteristics for imaging. The diagnosis is made on histological examination of the surgical specimen or biopsies. Radiotherapy and chemotherapy complete the treatment. The authors report the case of a 26-year-old patient who only had pelvic discomfort. Diagnostic laparoscopy showed a retroperitoneal and retrovesical mass of five centimeters. The patient benefited from adjuvant chemotherapy and radiotherapy. She is free of disease 30 months after treatment.

Keywords

Primitive neuroectodermal tumor; PNET; Retroperitoneal; Ewing’s tumor.

Cite and Share

A. Koch, S. Frigo, L. Lecointre,M. Humme,C.Y. Akladios,J.P. Bergerat,G. Noë,A. Wattiez. Retroperitoneal primitive neuroectodermal tumor (PNET): case report and review of literature. European Journal of Gynaecological Oncology. 2017. 38(2);314-318.

References

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