Malignant struma ovarii with synchronous papillary thyroid carcinoma: a rare diagnosis

Struma ovarii is a rare form of ovarian tumor, represented in more than 50% by thyroid tissue. Malignant transformation is a rare presentation and comprises about 5% of cases. The authors report a female with papillary thyroid carcinoma arising in struma ovarii, diagnosed after surgery for a right ovarian mass. Thyroid examination showed two nodular lesions in the left lobe. Total thyroidect my was performed and histology showed a papillary carcinoma, discordant in terms of ovarian tissue, synchronous to the ovary. Radioiodine ablation of residual thyroid tissue was performed and levothyroxine mildly-suppressive treatment was begun. Although the rareness of association, it is of extreme importance that patients with malignant struma ovarii undergo imaging of thyroid gland for study of coexistent disease.

Ovarian neoplasm; Struma ovarii; Thyroid neoplasm; Ovarian teratoma

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