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Intrapelvic sclerosing epithelioid fibrosarcoma: a case report

  • M. Omori1,*,
  • S. Ichikawa2
  • M. Oi1
  • T. Inoue3
  • M. Ohgi1
  • H. Fukasawa1
  • A. Hashi1
  • S. Hirata1

1Department of Obstetrics and Gynecology, Faculty of Medicine, University of Yamanashi, Japan

2Department of Radiology, Faculty of Medicine, University of Yamanashi, Yamanashi, Japan

3Department of Pathology, Faculty of Medicine, University of Yamanashi, Yamanashi, Japan

DOI: 10.12892/ejgo4241.2018 Vol.39,Issue 6,December 2018 pp.1028-1031

Published: 15 December 2018

*Corresponding Author(s): M. Omori E-mail: msasaki@yamanashi.ac.jp

Abstract

Sclerosing epithelioid fibrosarcoma (SEF) is a rare deep-seated tumor, that typically develops in the lower extremity, limb girdle, and trunk. This tumor is clinically aggressive, with a poor prognosis. The authors present an extremely rare case of SEF developing in the pelvis. The patient was a 75-year-old woman presenting with a solid mass located adjacent to the uterus in the left adnexal region on vaginal ultrasonography. MRI showed a lobulated solid mass exhibiting hypointensity on T1- and T2-weighted imaging. The tumor also showed heterogeneous signal intensity on diffusion-weighted imaging, and heterogeneous enhancement on dynamic study, and both features were distinct in the tumor’s peripheral zone. These MRI features were correlated with more hypercellularity in the peripheral zone on histology. To date, few reports have focused on the MRI features of SEF. Diffusion-weighted and contrast-enhanced MRI may provide more useful information for the diagnosis of SEF located in uncommon sites.

Keywords

Fibrosarcoma; Sclerosing epithelioid fibrosarcoma; Pelvic mass; Magnetic resonance imaging; Immunohistochemistry.

Cite and Share

M. Omori,S. Ichikawa,M. Oi,T. Inoue,M. Ohgi,H. Fukasawa,A. Hashi,S. Hirata. Intrapelvic sclerosing epithelioid fibrosarcoma: a case report. European Journal of Gynaecological Oncology. 2018. 39(6);1028-1031.

References

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