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Case Reports

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Perivascular epithelioid cell tumor arising in the left parametriu a case report

  • Soo-Young Lee1
  • Dae-Hyung Lee1,*,

1Department of Obstetrics & Gynecology, College of Medicine, Yeungnam University Medical Center, Daegu, Republic of Korea

DOI: 10.31083/j.ejgo.2020.04.5458 Vol.41,Issue 4,August 2020 pp.657-660

Submitted: 06 January 2020 Accepted: 17 June 2020

Published: 15 August 2020

*Corresponding Author(s): Dae-Hyung Lee E-mail: leebhy@ynu.ac.kr

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Abstract

The perivascular epithelioid cell tumors (PEComas) mimic rare epithelial mesenchymal tumors with epithelioid features and perivascular clear cells that co-express the muscle and melanocytic markers. The PEComas include lymphangioleiomyomatosis, clear cell sugar tumor, angiomyolipoma, and myomelanocytic tumors. We report a case involving 37-year-old woman with a PEComa in the left parametrium. The patient was referred to our hospital with an adnexal tumor detected during medical examination. Therefore, she underwent laparoscopic mass excision surgery. Immunohistochemical staining of the tumor cells indicated positivity for Melan A, HMB45, and desmin. Finally, the tumor was diagnosed as a PEComa. The patient is undergoing regular follow-up, and no recurrence has been noted at 2 years after the surgery.

Keywords

Perivascular epithelioid cell tumors; Parametrium; Immunohistochemistry

Cite and Share

Soo-Young Lee,Dae-Hyung Lee. Perivascular epithelioid cell tumor arising in the left parametriu a case report. European Journal of Gynaecological Oncology. 2020. 41(4);657-660.

URL:

https://www.ejgo.net/articles/10.31083/j.ejgo.2020.04.5458

References

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